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| Ambiguous clear cell carcinoma in medullary sponge kidney: A case report |
Yang Chen,Tianyu Li( ),Jiwen Cheng()
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| Department of Urology, The First Affiliated Hospital of Guangxi Medical University, Nanning, China |
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Abstract Medullary sponge kidney (MSK) is a characteristic renal malformation, with a relatively low incidence. Radiologically, identification of MSK is sometimes ambiguous when compared to a renal mass. Here, we report a novel renal clear cell carcinoma in MSK, and discuss our approach to treatment. We recommended that a preoperative biopsy should be performed, followed by a comprehensive discussion regarding the appropriate perioperative preparations and careful surgical techniques that should be performed for this complex disease.
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Received: 28 November 2018
Available online: 13 September 2019
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Corresponding Authors:
Tianyu Li,Jiwen Cheng
E-mail: mcphung@gmail.com;chengjiwen1977@foxmail.com
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The radiological image in the computed tomography (CT) and kidney urinary bladder (KUB) radiograph. (A and B) Transverse section of the CT in excretory phase shows medullary cyst in the right kidney; (C) The Urinary tract plain X-ray has the characteristic appearance of a “bouquet of flowers” (We did not deal with the renal colic for without evident obstruction; postoperatively, two double-J ureteral stents were indwelling in bilateral ureters to keep the ureter open).
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The figures of computed tomography in unenhanced phase (A), arterial phase (B), venous phase (C) and excretory phase (D) identified a mass in the right kidney. In four phases, the CT values were similar (unenhanced phase: 29 for renal parenchyma, 32 for mass; arterial phase: 90 for renal parenchyma, 93 for mass; venous phase: 127 for renal parenchyma, 106 for mass; excretory phase: 69 for renal parenchyma, 67 for mass).
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The gross pathology of tumor tissues. The tumor was removed integrally, without obvious capsule (A). When incising the tumor, the sarcodous tissues were shown (B).
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| Author | Date | Country | Title | Case number | Year | Gender | Journal | | Kaver et al. [13] | 1989 | United States | Segmental medullary sponge kidney mimicking a renal mass. | 1 | 55 | female | J Urol | | Choong and Phillips [17] | 1991 | Australia | Renal transitional cell carcinoma mimicking medullary sponge kidney. | 1 | 68 | male | Br J Radiol | | Fellegara et al. [16] | 2005 | Italy | A case of medullary sponge kidney (Cacchi-Ricci disease) mimicking a renal mass. | 1 | 46 | male | Arch Ital Urol Androl |
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Previous literatures about the medullary sponge kidney and renal massa.
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